Abstract
Until recently, the recommendation for primary retroperitoneal sarcomas (RPS) was
to perform a complete en-bloc gross excision, (neo) adjuvant treatments being options
which were not validated by randomized studies, with a large discrepancy of use between
centers. The heterogeneity of RPS, with their different biological behaviour, renders
a homogenous therapeutic and surgical approach probably inappropriate. Recent studies,
both surgical and dedicated to adjuvant treatments, allow refining these recommendations.
This review summarizes recent advances and directions.
Keywords
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Article info
Publication history
Published online: May 16, 2022
Accepted:
May 11,
2022
Received in revised form:
May 2,
2022
Received:
February 3,
2022
Identification
Copyright
© 2022 Elsevier Ltd, BASO ~ The Association for Cancer Surgery, and the European Society of Surgical Oncology. All rights reserved.
